Dr Georg Von Jonquieres

Contact Details

Phone: +61 2 9385 2376
Email: g.jonquieres@unsw.edu.au

Tabs

Main

University role:

Postdoctoral Fellow

Research

Teaching & Supervision

I am available to supervise:

Yes

Publications related to this Person

Journal articles

Broccoli L; Uhrig S; von Jonquieres G; Schönig K; Bartsch D; Justice NJ; Spanagel R; Sommer WH; Klugmann M; Hansson AC, 2018, 'Targeted overexpression of CRH receptor subtype 1 in central amygdala neurons: effect on alcohol-seeking behavior', Psychopharmacology, vol. 235, pp. 1821 - 1833, http://dx.doi.org/10.1007/s00213-018-4908-6

Powell KL; Fitzgerald X; Shallue C; Jovanovska V; Klugmann M; Von Jonquieres G; O'Brien TJ; Morris MJ, 2018, 'Gene therapy mediated seizure suppression in Genetic Generalised Epilepsy: Neuropeptide Y overexpression in a rat model', Neurobiology of Disease, vol. 113, pp. 23 - 32, http://dx.doi.org/10.1016/j.nbd.2018.01.016

von Jonquieres G; Spencer ZHT; Rowlands BD; Klugmann CB; Bongers A; Harasta AE; Parley KE; Cederholm J; Teahan O; Pickford R, 2018, 'Uncoupling N-acetylaspartate from brain pathology: implications for Canavan disease gene therapy', Acta Neuropathologica, vol. 135, pp. 95 - 113, http://dx.doi.org/10.1007/s00401-017-1784-9

Datko MC; Hu JH; Williams M; Reyes CM; Lominac KD; von Jonquieres G; Klugmann M; Worley PF; Szumlinski KK, 2017, 'Behavioral and neurochemical phenotyping of mice incapable of homer1a induction', Frontiers in Behavioral Neuroscience, vol. 11, http://dx.doi.org/10.3389/fnbeh.2017.00208

Bi M; Gladbach A; Van Eersel J; Ittner A; Przybyla M; Van Hummel A; Chua SW; Hoven JVD; Lee WS; Müller J, 2017, 'Tau exacerbates excitotoxic brain damage in an animal model of stroke', Nature Communications, vol. 8, http://dx.doi.org/10.1038/s41467-017-00618-0

Georgiou E; Sidiropoulou K; Richter J; Papaneophytou C; Sargiannidou I; Kagiava A; Von Jonquieres G; Christodoulou C; Klugmann M; Kleopa KA, 2017, 'Gene therapy targeting oligodendrocytes provides therapeutic benefit in a leukodystrophy model', Brain, vol. 140, pp. 599 - 616, http://dx.doi.org/10.1093/brain/aww351

Szumlinski KK; Lominac KD; Campbell RR; Cohen M; Fultz EK; Brown CN; Miller BW; Quadir SG; Martin D; Thompson AB, 2017, 'Methamphetamine Addiction Vulnerability: The Glutamate, the Bad, and the Ugly', Biological Psychiatry, vol. 81, pp. 959 - 970, http://dx.doi.org/10.1016/j.biopsych.2016.10.005

Fröhlich D; Suchowerska AK; Spencer ZHT; von Jonquieres G; Klugmann CB; Bongers A; Delerue F; Stefen H; Ittner LM; Fath T, 2017, 'In vivo characterization of the aspartyl-tRNA synthetase DARS: Homing in on the leukodystrophy HBSL', Neurobiology of Disease, vol. 97, pp. 24 - 35, http://dx.doi.org/10.1016/j.nbd.2016.10.008

O'Brien R; Tran SL; Maritz MF; Liu B; Kong CF; Purgato S; Yang C; Murray J; Russell AJ; Flemming CL, 2016, 'MYC-driven neuroblastomas are addicted to a telomerase-independent function of dyskerin', Cancer Research, vol. 76, pp. 3604 - 3617, http://dx.doi.org/10.1158/0008-5472.CAN-15-0879

Harasta AE; Power JM; Von Jonquieres G; Karl T; Drucker DJ; Housley GD; Schneider M; Klugmann M, 2015, 'Septal glucagon-like peptide 1 receptor expression determines suppression of cocaine-induced behavior', Neuropsychopharmacology, vol. 40, pp. 1969 - 1978, http://dx.doi.org/10.1038/npp.2015.47

Gould AT; Sacramento AD; Wroten MG; Miller BW; Von Jonquieres G; Klugmann M; Ben-Shahar O; Szumlinski KK, 2015, 'Cocaine-elicited imbalances in ventromedial prefrontal cortex Homer1 versus Homer2 expression: Implications for relapse', Addiction Biology, vol. 20, pp. 148 - 157, http://dx.doi.org/10.1111/adb.12088

Von Jonquieres G; Froud KE; Klugmann CB; Wong ACY; Housley GD; Klugmann M, 2014, 'Loss of central auditory processing in a mouse model of canavan disease', PLoS ONE, vol. 9, http://dx.doi.org/10.1371/journal.pone.0097374

von Jonquieres G; Klugmann C; Harrasta A; Klugmann M, 2013, 'DEVELOPMENT OF RAAV VECTORS FOR THE TREATMENT OF LEUKODYSTROPHIES', CYTOTHERAPY, vol. 15, pp. S33 - S33, http://dx.doi.org/10.1016/j.jcyt.2013.01.125

Jonquieres G; Mersmann N; Teahan O; Klugmann CB; Harasta AE; Lutz B; Housley GD; Klugmann M, 2013, 'AAV-BASED GENE THERAPY APPROACHES FOR THE TREATMENT OF CANAVAN DISEASE', CYTOTHERAPY, vol. 15, pp. S12 - S12, http://dx.doi.org/10.1016/j.jcyt.2013.01.042

Cozzoli DK; Finn DA; Courson J; Wroten MG; Greentree DI; Lum EN; Campbell RR; Thompson AB; Maliniak D; Szumlinski KK, 2013, 'Binge Alcohol Drinking by Mice Requires Intact Group1 Metabotropic Glutamate Receptor Signaling Within the Central Nucleus of the Amygdale', Neuropsychopharmacology, http://dx.doi.org/10.1038/npp.2013.214

Obara I; Goulding SP; Gould AT; Lominac KD; Hu JH; Zhang PW; von Jonquieres G; Dehoff M; Xiao B; Seeburg PH, 2013, 'Homers at the interface between reward and pain', Frontiers in Psychiatry, vol. 4

von Jonquieres G; Mersmann N; Klugmann CB; Harasta AE; Lutz B; Teahan O; da Housley G; Fröhlich D; Krämer-Albers EM; Klugmann M, 2013, 'Glial Promoter Selectivity following AAV-Delivery to the Immature Brain', PLoS ONE, vol. 8, http://dx.doi.org/10.1371/journal.pone.0065646

Ary AW; Lominac KD; Wroten MG; Williams AR; Campbell RR; Ben-Shahar O; von Jonquieres G; Klugmann M; Szumlinski KK, 2013, 'Imbalances in prefrontal cortex CC-Homer1 versus CC-Homer2 expression promote cocaine preference', Journal of Neuroscience, vol. 33, pp. 8101 - 8113, http://dx.doi.org/10.1523/JNEUROSCI.1727-12.2013

Thoms JAI; Birger Y; Foster S; Knezevic K; Kirschenbaum Y; Chandrakanthan V; Jonquieres G; Spensberger D; Wong JW; Oram SH, 2011, 'ERG promotes T-acute lymphoblastic leukemia and is transcriptionally regulated in leukemic cells by a stem cell enhancer', Blood, vol. 117, pp. 7079 - 7089, http://dx.doi.org/10.1182/blood-2010-12-317990

Marshall GM; Gherardi S; Xu N; Neiron Z; Trahair T; Scarlett CJ; Chang DK; Liu PY; Jankowski K; Iraci N, 2010, 'Transcriptional upregulation of histone deacetylase 2 promotes Myc-induced oncogenic effects', Oncogene, vol. 29, pp. 5957 - 5968, http://dx.doi.org/10.1038/onc.2010.332

Von Jonquieres G, 2010, 'Transcriptional upregulation of histone deacetylase 2 promotes Myc-induced oncogenic effects', Oncogene, vol. 29, pp. 5957 - 5968, http://dx.doi.org/10.1038/onc.2010.332

Eckstein N; Servan K; Hildebrandt B; Pölitz A; Von Jonquières G; Wolf-Kümmeth S; Napierski I; Hamacher A; Kassack MU; Budczies J, 2009, 'Hyperactivation of the insulin-like growth factor receptor I signaling pathway Is an essential event for cisplatin resistance of ovarian cancer cells', Cancer Research, vol. 69, pp. 2996 - 3003, http://dx.doi.org/10.1158/0008-5472.CAN-08-3153

Eckstein N; Servan K; Girard L; Cai D; Von Jonquieres G; Jaehde U; Kassack MU; Gazdar AF; Minna JD; Royer HD, 2008, 'Epidermal growth factor receptor pathway analysis identifies amphiregulin as a key factor for cisplatin resistance of human breast cancer cells', Journal of Biological Chemistry, vol. 283, pp. 739 - 750, http://dx.doi.org/10.1074/jbc.M706287200

Gosepath EM; Eckstein N; Hamacher A; Servan K; Von Jonquieres G; Lage H; Györffy B; Royer HD; Kassack MU, 2008, 'Acquired cisplatin resistance in the head-neck cancer cell line Cal27 is associated with decreased DKK1 expression and can partially be reversed by overexpression of DKK1', International Journal of Cancer, vol. 123, pp. 2013 - 2019, http://dx.doi.org/10.1002/ijc.23721

von Jonquieres G; Fröhlich D; Klugmann CB; Wen X; Harasta AE; Ramkumar R; Spencer ZHT; Housley GD; Klugmann M, 'Recombinant Human Myelin-Associated Glycoprotein Promoter Drives Selective AAV-Mediated Transgene Expression in Oligodendrocytes', Frontiers in Molecular Neuroscience, vol. 9, http://dx.doi.org/10.3389/fnmol.2016.00013

Conference Papers

Georgiou E; Kagiava A; Sidiropoulou K; Richter J; Sargiannidou I; Papaneophytou C; von Jonquieres G; Christodoulou C; Klugmann M; Kleopa K, 2016, 'Gene delivery to oligodendrocytes re-establishes gap junctions and rescues a hypomyelinating leukodystrophy model', in EUROPEAN JOURNAL OF NEUROLOGY, WILEY, pp. 694 - 695, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000431634203169&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1

von Jonquieres G; Klugmann C; Harrasta A; Klugmann M, 2013, 'DEVELOPMENT OF rAAV VECTORS FOR THE TREATMENT OF LEUKODYSTROPHIES', in JOURNAL OF GENE MEDICINE, WILEY-BLACKWELL, Univ Technol, Sydney, AUSTRALIA, pp. 334 - 335, presented at 8th Meeting of the Australasian-Gene-Therapy-Society, Univ Technol, Sydney, AUSTRALIA, 08 - 10 May 2013, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000325102500046&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1

Kumari A; Richards LA; Jonquieres G; Knezevic K; O'Brien R; Napier CE; Marks-Bluth J; Pickett H; Pimanda JE; MacKenzie KL, 2012, 'Dyskerin Is Upregulated During Erythroid Differentiation of Human Hematopoietic Progenitor Cells and Hyperactivates Telomerase in Erythroid Precursor Cells', in BLOOD, AMER SOC HEMATOLOGY, Atlanta, GA, presented at 54th Annual Meeting and Exposition of the American-Society-of-Hematology (ASH), Atlanta, GA, 08 - 11 December 2012, http://dx.doi.org/10.1182/blood.V120.21.980.980

Conference Abstracts

von Jonquieres G; Klugmann C; Frohlich D; Housley GD; Klugmann M, 2018, 'NOVEL APPROACHES TO PREVENT THE NAASTY - TARGETED GENE THERAPY FOR LEUKODYSTROPHIES', in JOURNAL OF GENE MEDICINE, WILEY, Univ Technol Sydney, Sydney, AUSTRALIA, Vol. 20, presented at Joint 10th Annual Scientific Meeting of the Australian-Gene-and-Cell-Therapy-Society (AGCTS) and Australasian-Society-for-Stem-Cell-Research (ASSCR), Univ Technol Sydney, Sydney, AUSTRALIA, 24 - 26 May 2017, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000426528300030&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1

Perera C; Von Jonquieres G; Pinyon J; Parley K; Cederholm J; Julien J-P; Ryan A; Housley G, 2016, 'Phenotyping the differential innervation of the peripherin knockout mouse cochlea', in Proceedings of the Australian Physiological Society, Australian Physiological Society, Adelaide, presented at Australian Physiological Society, Adelaide, 04 - 07 December 2016

Jonquieres GV; Mersmann N; Klugmann C; Harrasta A; Klugmann M, 2015, 'Targeting oligodendrocytes in rAAV mediated gene replacement therapy for Canavan disease', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, Cairns, AUSTRALIA, Vol. 134, pp. 289 - 289, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australa, Cairns, AUSTRALIA, 23 - 27 August 2015, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300729&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1

Harrison-Tikisci Z; von Jonquieres G; Rowlands B; Klugmann C; Delarue F; Ittner L; Pickford R; Housley G; Rae C; Klugmann M, 2015, 'N-acetylaspartate: genomics, phenomics and metabonomics', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, Cairns, AUSTRALIA, Vol. 134, pp. 141 - 141, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australa, Cairns, AUSTRALIA, 23 - 27 August 2015, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300323&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1

Harasta A; Power JM; von Jonquieres G; Karl T; Drucker DJ; Housley GD; Schneider M; Klugmann M, 2015, 'Septal glucagon-like peptide 1 receptor expression determines suppression of cocaine-induced behaviour', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, Cairns, AUSTRALIA, Vol. 134, pp. 214 - 214, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australa, Cairns, AUSTRALIA, 23 - 27 August 2015, http://gateway.webofknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300522&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1